Akinetic‐rigid syndrome in a 13‐year‐old girl with HIV‐related progressive multifocal leukoencephalopathy
Identifieur interne : 005E25 ( Main/Exploration ); précédent : 005E24; suivant : 005E26Akinetic‐rigid syndrome in a 13‐year‐old girl with HIV‐related progressive multifocal leukoencephalopathy
Auteurs : Singer [États-Unis] ; Joseph R. Berger [États-Unis] ; Brian C. Bowen [États-Unis] ; Jocelyn H. Bruce [États-Unis] ; William J. Weiner [États-Unis]Source :
- Movement Disorders [ 0885-3185 ] ; 1993.
English descriptors
- KwdEn :
- AIDS-Related Opportunistic Infections (diagnosis), AIDS-Related Opportunistic Infections (pathology), Acquired immunodeficiency syndrome, Adolescent, Akinetic‐rigid syndrome, Basal ganglia diseases, Biopsy, Bradykinesia, Brain (pathology), Female, Humans, Leukoencephalopathy, Progressive Multifocal (diagnosis), Leukoencephalopathy, Progressive Multifocal (pathology), Magnetic Resonance Imaging, Magnetic resonance imaging, Movement Disorders (diagnosis), Movement Disorders (pathology), Muscle Rigidity (diagnosis), Muscle Rigidity (pathology), Myelin Sheath (pathology), Neurologic Examination, Parkinsonism, Progressive multifocal leukoencephalopathy.
- MESH :
- diagnosis : AIDS-Related Opportunistic Infections, Leukoencephalopathy, Progressive Multifocal, Movement Disorders, Muscle Rigidity.
- pathology : AIDS-Related Opportunistic Infections, Brain, Leukoencephalopathy, Progressive Multifocal, Movement Disorders, Muscle Rigidity, Myelin Sheath.
- Adolescent, Biopsy, Female, Humans, Magnetic Resonance Imaging, Neurologic Examination.
Abstract
A 13‐year‐old HIV‐ infected girl presented with a rapidly progressive akineticrigid syndrome. Cranial magnetic resonance imaging revealed bilateral centrum semiovale lesions extending into the basal ganglia. Detailed histopathological study of a biopsy specimen from the involved regions resulted in a diagnosis of progressive multifocal leukoencephalopathy (PML). This case illustrates that an akinetic‐rigid syndrome may be a rare presentation of PML. HIV‐related PML may have unusual radiological features. Brain biopsy may be necessary to confirm PML in cases associated with atypical clinical and radiological presentations.
Url:
DOI: 10.1002/mds.870080120
Affiliations:
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Le document en format XML
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<term>Adolescent</term>
<term>Akinetic‐rigid syndrome</term>
<term>Basal ganglia diseases</term>
<term>Biopsy</term>
<term>Bradykinesia</term>
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<term>Muscle Rigidity (diagnosis)</term>
<term>Muscle Rigidity (pathology)</term>
<term>Myelin Sheath (pathology)</term>
<term>Neurologic Examination</term>
<term>Parkinsonism</term>
<term>Progressive multifocal leukoencephalopathy</term>
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<front><div type="abstract" xml:lang="en">A 13‐year‐old HIV‐ infected girl presented with a rapidly progressive akineticrigid syndrome. Cranial magnetic resonance imaging revealed bilateral centrum semiovale lesions extending into the basal ganglia. Detailed histopathological study of a biopsy specimen from the involved regions resulted in a diagnosis of progressive multifocal leukoencephalopathy (PML). This case illustrates that an akinetic‐rigid syndrome may be a rare presentation of PML. HIV‐related PML may have unusual radiological features. Brain biopsy may be necessary to confirm PML in cases associated with atypical clinical and radiological presentations.</div>
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