Movement Disorders (revue)

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Akinetic‐rigid syndrome in a 13‐year‐old girl with HIV‐related progressive multifocal leukoencephalopathy

Identifieur interne : 005E25 ( Main/Exploration ); précédent : 005E24; suivant : 005E26

Akinetic‐rigid syndrome in a 13‐year‐old girl with HIV‐related progressive multifocal leukoencephalopathy

Auteurs : Singer [États-Unis] ; Joseph R. Berger [États-Unis] ; Brian C. Bowen [États-Unis] ; Jocelyn H. Bruce [États-Unis] ; William J. Weiner [États-Unis]

Source :

RBID : ISTEX:01E26B79C4A2CDCAED8C899A7F48E59BD2DEE9A3

English descriptors

Abstract

A 13‐year‐old HIV‐ infected girl presented with a rapidly progressive akineticrigid syndrome. Cranial magnetic resonance imaging revealed bilateral centrum semiovale lesions extending into the basal ganglia. Detailed histopathological study of a biopsy specimen from the involved regions resulted in a diagnosis of progressive multifocal leukoencephalopathy (PML). This case illustrates that an akinetic‐rigid syndrome may be a rare presentation of PML. HIV‐related PML may have unusual radiological features. Brain biopsy may be necessary to confirm PML in cases associated with atypical clinical and radiological presentations.

Url:
DOI: 10.1002/mds.870080120


Affiliations:


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Le document en format XML

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<term>Basal ganglia diseases</term>
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<term>Movement Disorders (pathology)</term>
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<term>Muscle Rigidity (pathology)</term>
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